Agenesia pulmonar unilateral maura cavada malcon, claudio mattar malcon, marina neves cavada, paulo eduardo macedo caruso, lara florio real abstract pulmonary agenesis is a rare congenital anomaly. Agenesia pulmonar unilateral unilateral pulmonary agenesis. Em 50% dos casos, principalmente naqueles com agenesia pulmonar a direita, estao associadas malformacoes cardiovasculares, musculoesqueleticas. Volume 77, issue 3, julyseptember 2014, pages 1282. The patient died six days after birth and necropsy confirmed pulmonary agenesis. It is distinguished from pulmonary agenesis, although similar, the main difference being that there is a shortblind ending bronchus in aplasia 3 it is usually unilateral, as bilateral pulmonary aplasia is. Pulmonary aplasia is a rare congenital pathology in which there is unilateral or bilateral absence of lung tissue. O ecodopplercardiograma revelou agenesia da arteria pulmonar esquerda, sem outras alteracoes cardiacas, e a broncoscopia demonstrou ausencia completa do pulmao esquerdo e inexistencia do coto bronquico. We are reporting an additional case of an agenesis of the lung.
It is distinguished from pulmonary agenesis, although similar, the main difference being that there is a shortblind ending bronchu. Report of case a 2day old baby girl was seen by one of us b. A agenesia pulmonar e uma malformacao congenita rara, consistindo na ausencia completa do parenquima pulmonar, bronquios e vasos pulmonares. We report the case of an 8yearold boy with left lung agenesis, without any other congenital malformations. Completa agenesia traqueal, con bronquios y carina normales. The frequency with which one encounters other malformations in patients with pulmonary agenesis has led ferguson and neuhauser to explain the genesis of this. Agenesia pulmonar revista javeriana pontificia universidad. Congenital pulmonary agenesis diseases of the chest. Tetralogy of fallot with absent pulmonary valve revista portuguesa. Feb 27, 2019 download pdf copy by sally robertson, b. Residencia pediatrica agenesia pulmonar associada a. Pdf a agenesia pulmonar e uma anomalia congenita rara. Li com bastante interesse e congratulo os autores malcon et al.